PReS-FINAL-2359: Renal involvement in hypocomplementemic urticarial vasculitis syndrome (huvs): report of 3 paediatric cases
نویسندگان
چکیده
Introduction HUVS is a rare disease characterized by persistent urticarial lesions with histological evidence of leucocytoclastic vasculitis and complement activation with a marked decrease in circulating C1q levels. HUVS can present systemic features involving the musculoskeletal, pulmonary, renal and gastrointestinal systems; its peak incidence is in the fifth decade of life. The exact prevalence of HUVS in children is unknown.
منابع مشابه
Hypocomplementemic urticarial vasculitis: a rare presentation of systemic lupus erythematosus.
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